Dermatomyositis associated with generalized subcutaneous edema and Evans syndrome

Kyu Dong Jung, Pyoung Su Kim, Hae Young Park, Cho Rok Kim, Ji Yeon Byun, Dong Youn Lee, Joo Heung Lee, Jun Mo Yang, Eil Soo Lee

Research output: Contribution to journalReview articlepeer-review

15 Scopus citations

Abstract

Although periorbital edema is a common manifestation of dermatomyositis (DM), generalized subcutaneous edema associated with DM is extremely rare. Evans syndrome is an autoimmune disease in which an individual's antibodies attack one's own red blood cells and platelets. Evans syndrome is rarely a presenting feature of DM. DM has been rarely reported to be associated with either generalized edema or Evans syndrome. We report the case of a 52-year-old Korean woman who presented with generalized subcutaneous edema, an erythematous rash, dysphagia, and proximal muscle weakness, and subsequently developed features of Evans syndrome. Treatment with high-dose glucocorticoids and an immunosuppressive agent controlled the DM, the generalized subcutaneous edema, and the Evans syndrome.

Original languageEnglish
Pages (from-to)144-147
Number of pages4
JournalJournal of the American Academy of Dermatology
Volume66
Issue number1
DOIs
StatePublished - Jan 2012

Keywords

  • Evans syndrome
  • dermatomyositis
  • generalized edema

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